Eating themselves to death: have "personal rights" gone too far in treating people with Prader-Willi syndrome?
نویسندگان
چکیده
In contrast to even a decade ago, giant steps have been made toward increased community inclusion, choice, and self-determination for persons with mental retardation. As workers put these goals into practice, they are sometimes faced with uncomfortable exceptions to the rule: persons for whom increased decision-making leads to unhealthy and even life-threatening consequences. Prader-Willi syndrome is one such exception.
منابع مشابه
Dental Management of Patients with Prader Willi Syndrome
Prader–Willi syndrome (PWS) is a genetic disorder which occurs with a frequency of about one in 10,000–30,000 live newborns. Both males and females, and all races are equally affected. PWS is a complex disorder with multiple disabilities, and the main defect is found in the hypothalamus. Child with PWS at the age between 2 and 3 years becomes constantly hungry and if the diet is not controlled,...
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A central characteristic of people with Prader-Willi Syndrome (PWS) is an apparent insatiable appetite leading to severe overeating and the potential for marked obesity and associated serious health problems and premature death. This behaviour may be due to the effects of the genetic defect resulting from the chromosome 15 abnormalities associated with the syndrome. We examine the ethical and l...
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Since the original description by Prader, Labhart, and Willi in 1956,' there have been over 700 case reports of the Prader-Willi syndrome and by the end of 1991 the PraderWilli Association were aware of 1595 affected individuals in North America.2 Estimates of prevalence vary: one group has reported a consensus figure of one in 10 000 births,3 but with modem techniques for laboratory diagnosis ...
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BACKGROUND This three-part study examines previous clinical impressions that people with Prader-Willi syndrome have unusual jigsaw puzzle and word search skills. RESULTS Children with Prader-Willi syndrome showed relative strengths on standardized visual-spatial tasks (Object Assembly, Triangles, VMI) in that their scores were significantly higher than age- and IQ-matched peers with mixed men...
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Prader–Willi syndrome (PWS) is a genetic disorder due to loss of function of specific genes on chromosome 15. It occurs in males and females, no matter what race. As an infant, PWS shows itself in weak muscle tone (hypotonia, Pic. 1), feeding difficulties, poor growth, and delayed development. In the beginning during childhood, characterizes itself by having the kids develop an insatiable appet...
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ورودعنوان ژورنال:
- Mental retardation
دوره 35 4 شماره
صفحات -
تاریخ انتشار 1997